A Case of Primary Endobronchial Leiomyosarcoma Noticed by Massive Hemoptysis.

Kim, Woo Youl; Kang, Gu Hyun; Lee, Jin Ho; Park, Sun Hyo; Kang, Kyung Woo

doi:2006.61.5.484

Tuberc Respir Dis > Volume 61(5); 2006 > Article

Case Report

Tuberculosis and Respiratory Diseases 2006;61(5):484-489.
DOI: https://doi.org/10.4046/trd.2006.61.5.484 Published online November 1, 2006.

A Case of Primary Endobronchial Leiomyosarcoma Noticed by Massive Hemoptysis.

Woo Youl Kim, Gu Hyun Kang, Jin Ho Lee, Sun Hyo Park, Kyung Woo Kang

Division of Pulmonary and Critical Care Medicine, Department of Internal Medicine, Masan Samsung Hospital, Sungkyunkwan University School of Medicine, Masan, Korea. kangkw9@naver.com

Abstract

A primary pulmonary leiomyosarcoma is a very rare pulmonary malignancy that arises from smooth muscle of either the bronchial or arterial walls. Common symptoms of the tumor are cough, dyspnea, chest pain and hemoptysis. The diagnosis of a primary pulmonary sarcoma can be established only after extensive clinical and radiologic examinations have failed to identify an alternative primary source. The only effective treatment for the tumor is a complete surgical resection when feasible. The type of resection is dictated by the local anatomic extent of the tumor. We report a case of a 21-year-old male with a primary endobronchial leiomyosarcoma who presented with massive hemoptysis. A necrotic ulcerative endobronchial lesion was observed in the orifice of left lower lobe bronchus on a bronchoscopic examination. He was treated with a complete sleeve resection of the left lower lobe. Three months later, local recurrence of the tumor was noticed on the follow up bronchoscopy and a then left pneumonectomy was then performed. Fifteen months later, the patient died from empyema with a bronchopleural fistula that was associated with tumor recurrence at the stump of the pneumonectomy.

Key Words: Endobronchial leiomyosarcoma, Surgical resection