A Case of Pulmonary Metastasis of a Dermatofibrosarcoma Protuberans.

Jung, Se Jin; Byun, Min Kwang; Chung, Woo Young; Park, Moo Suk; Kang, Shin Myung; Kim, Hae Ryoung; Shin, Dong Hwan; Kim, Se Kyu; Chang, Joon; Kim, Sung Kyu; Kim, Young Sam

doi:2006.61.6.573

Tuberc Respir Dis > Volume 61(6); 2006 > Article

Case Report

Tuberculosis and Respiratory Diseases 2006;61(6):573-577.
DOI: https://doi.org/10.4046/trd.2006.61.6.573 Published online December 1, 2006.

A Case of Pulmonary Metastasis of a Dermatofibrosarcoma Protuberans.

Se Jin Jung, Min Kwang Byun, Woo Young Chung, Moo Suk Park, Shin Myung Kang, Hae Ryoung Kim, Dong Hwan Shin, Se Kyu Kim, Joon Chang, Sung Kyu Kim, Young Sam Kim

¹Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea. ysamkim@yumc.yonsei.ac.kr
²The Institute of Chest Diseases, Yonsei University College of Medicine, Seoul, Korea.
³Department of Pathology, Yonsei University College of Medicine, Seoul, Korea.

Abstract

Dermatofibrosarcoma protuberans (DFPS) is a locally aggressive skin tumor with a very low incidence in the general population. This tumor has a remarkable tendency to recur, However, a metastasis is rare. We report a case of DFPS with a pulmonary metastasis in 28-year-old man. The pulmonary metastasis developed 5 years after a complete resection of the primary skin tumor. We reviewed the clinical manifestations and treatment of DFPS, and highlight the need for a long-term follow-up examination for metastases after a wide excision of these lesions.

Key Words: Dermatofibrosarcoma protuberans, Pulmonary metastasis