Tuberc Respir Dis > Volume 64(2); 2008 > Article
Tuberculosis and Respiratory Diseases 2008;64(2):138-143.
DOI: https://doi.org/10.4046/trd.2008.64.2.138    Published online February 1, 2008.
A Case of Nonspecific Interstitial Pneumonia Complicated with Spontaneous Pneumomediastinum, Subcutaneous Emphysema and Pneumatosis Interstinalis.
Myung Jae Park
Department of Pulmonary and Critical Care Medicine, Kyung Hee University School of Medicine, Seoul, Korea. mjpwis@chol.com
Abstract
Pneumatosis intestinalis or spontaneous pneumomediastinum are rarely associated with nonspecific interstitial pneumonia (NSIP). However, the development of both conditions in the same patient simultaneously has not been reported previously. A 56-year-old man with NSIP developed spontaneous pneumomediastinum accompanied by subcutaneous emphysema and pneumatosis intestinalis after the treatment with intravenous high dose steroid. The development of spontaneous pneumomediastinum, subcutaneous emphysema and pneumatosis intestinalis in this patient was possibly due to the factors such as NSIP, high dose steroid therapy and subclinical dermatomyositis. Treatment with corticosteroid and cyclosporin gradually improved his exacerbated NSIP and pneumomediastinum, subcutaneous emphysema, pneumatosis intestinalis.
Key Words: Nonspecific interstitial pneumonia, Pneumatosis intestinalis, Pneumomediastinum


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