A Case of Wegener's Granulomatosis with Delayed Diagnosis due to Clinical Features of Henoch-Schonlein Purpura.

Song, Se Bin; Choi, Hye Sook; Kim, Yee Hyung; Choi, Cheon Woong; Park, Myung Jae; Yoo, Jee Hong; Kang, Hong Mo; Kim, Yoon Hwa; Par, Joo Cheol

doi:2007.63.6.531

Tuberc Respir Dis > Volume 63(6); 2007 > Article

Case Report

Tuberculosis and Respiratory Diseases 2007;63(6):531-536.
DOI: https://doi.org/10.4046/trd.2007.63.6.531 Published online December 1, 2007.

A Case of Wegener's Granulomatosis with Delayed Diagnosis due to Clinical Features of Henoch-Schonlein Purpura.

Se Bin Song, Hye Sook Choi, Yee Hyung Kim, Cheon Woong Choi, Myung Jae Park, Jee Hong Yoo, Hong Mo Kang, Yoon Hwa Kim, Joo Cheol Par

¹Department of Pulmonary and Critical Care Medicine, Kyunghee University College of Medicine, Seoul, Korea. kmcim@chol.com
²Department of Pathology, Kyunghee University College of Medicine, Seoul, Korea.
³Department of Thoracic Surgery, Kyunghee University College of Medicine, Seoul, Korea.

Abstract

Wegener's granulomatosis is a systemic vasculitis of the medium and small arteries, as well as of the venules, arterioles, and occasionally large arteries, and primarily involves the upper and lower respiratory tracts and the kidneys. Renal symptoms of Wegener's granulomatosis are indistinguishable from those of vasculitis such as Henoch-Schonlein purpura and microscopic polyangiitis. This case, though initially diagnosed as Henoch-Schonlein purpura, was confirmed as Wegener's granulomatosis from a lung biopsy fifteen years after the initial diagnosis. We report this case with a review of the literature.

Key Words: Wegener's granulomatosis, Henoch-Schonlein purpura