Localized Fibrosing Mediastinitis with Superior Vena Caval(SVC) Syndrome.

Shin, Sang Yun; Kim, Beom Kyung; Park, Byung Hoon; Park, Seon Cheol; Park, Jun Chul; Soon, Myoung Kyun; Lee, Seung Yul; Im, Eui; Jeon, Han Ho; Jung, Kyung Soo; Jeong, Jae Heon; Choi, Yu Ri; Kang, Kyoung Hoon; Choi, Yoon Jung; Hong, Yong Kook; Kim, Chong Ju

doi:2007.63.4.387

Tuberc Respir Dis > Volume 63(4); 2007 > Article

Case Report

Tuberculosis and Respiratory Diseases 2007;63(4):387-391.
DOI: https://doi.org/10.4046/trd.2007.63.4.387 Published online October 1, 2007.

Localized Fibrosing Mediastinitis with Superior Vena Caval(SVC) Syndrome.

Sang Yun Shin, Beom Kyung Kim, Byung Hoon Park, Seon Cheol Park, Jun Chul Park, Myoung Kyun Soon, Seung Yul Lee, Eui Im, Han Ho Jeon, Kyung Soo Jung, Jae Heon Jeong, Yu Ri Choi, Kyoung Hoon Kang, Yoon Jung Choi, Yong Kook Hong, Chong Ju Kim

¹Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital, Koyang, Korea. kom2d@netsgo.com
²Department of Thoracic surgery, National Health Insurance Corporation Ilsan Hospital, Koyang, Korea.
³Department of Pathology, National Health Insurance Corporation Ilsan Hospital, Koyang, Korea.
⁴Department of Radiology, National Health Insurance Corporation Ilsan Hospital, Koyang, Korea.
⁵Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea

Abstract

Fibrosing mediastinitis is a rare disease that is characterized by the proliferation of dense fibrous tissue of the mediastinum. The pathogenesis of fibrosing mediastinitis is unknown in most cases. However, histoplasmosis, tuberculosis, autoimmune disease, radiation therapy, and other idiopathic fibroinflammatory diseases have been implicated in some cases. Most clinical features are related to an obstruction or compression of the mediastinal structure. Fibrosing mediastinitis is often progressive and occurs diffusely throughout the mediastinum. We encountered a case of fibrosing mediastinitis of a very focal lesion without evidence of mediastinal involvement. The condition was confirmed by biopsy and graft bypass surgery was performed because of SVC syndrome.

Key Words: Fibrosing mediastinitis, Superior vena caval syndrome