Idiopathic Fibrosing Mediastinitis Causing Extensive Fibrotic Veno-occlusion with Minimal Mediastinal Involvement. |
Je Hyeong Kim, Gyu Young Hur, Seung Heon Lee, Sang Yeub Lee, Sang Myun Park, Chol Shin, Jae Jeong Shim, Kwang Ho In, Han Kyeom Kim, Kyung Ho Kang, Se Hwa Yoo |
1Department of Internal Medicine, College of Medicine, Korea University, Seoul, Korea. jaejshim@kumc.or.kr 2Department of Pathology, College of Medicine, Korea University, Seoul, Korea. 3Department of Internal Medicine, College of Medicine, Wonkwang University, Iksan, Korea. |
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Abstract |
A 68-year-old woman was admitted after suffering facial edema with neck vein engorgement ofr approximately 2 months. A chest X-ray showed a mild widening of the superior mediastinum and a luminal obliteration of the super ior vena cava (SVC) was noted on a computed tomograph. Venography showed that both subclavian veins were obstructed at the level of the poxima clavicle with a nonvisualization of the SVC. The SVC, both the innominate and the left inthrnal jugular veins were completely obstructed with extensive cord-like fibrotix changes despite the obsence of mediastinal involvement. The microscopic features showed a chronic granulomatous inflammation with a fibrosis minimally invading the mediastinal fat, which is cosistent with fibrosing mediastinitis. |
Key Words:
Fibrosing mediastinitis, Superior vena cave syndrome |
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