Myxoid Leiomyosarcoma of the Superior Vena Cava Syndrome.

Jung, Ki Hwan; Lee, Seung Heon; Kim, Byung Gyu; Kong, Hee Sang; Kim, Je Hyeong; Bak, Sang Myeon; Shin, Cheol; Shim, Jae Jeong; Kim, Han Gyum; In, Kwang Ho; Kang, Kyung Ho; Yoo, Se Hwa

doi:2001.51.2.173

Tuberc Respir Dis > Volume 51(2); 2001 > Article

Case Report

Tuberculosis and Respiratory Diseases 2001;51(2):173-177.
DOI: https://doi.org/10.4046/trd.2001.51.2.173 Published online August 1, 2001.

Myxoid Leiomyosarcoma of the Superior Vena Cava Syndrome.

Ki Hwan Jung, Seung Heon Lee, Byung Gyu Kim, Hee Sang Kong, Je Hyeong Kim, Sang Myeon Bak, Cheol Shin, Jae Jeong Shim, Han Gyum Kim, Kwang Ho In, Kyung Ho Kang, Se Hwa Yoo

Abstract

A 38-year-old woman presented with facial edema with neck vein engorgement for about 45 days. Chest roentgenography showed bulging soft tissue opacities in the right superoanterior mediastinum and a lobulated intraluminal mass was noted in the superior vena cava on the venacavogram. The superior vena cava was incised and the tumor located from the junction of the superior vena cava and internal jugular vein to the right atrial inlet was excised. Grossly, the tumor was myxoid or gelatinous in appearance. A combination of microscopic and immunohistochemical features showed myxoid leiomyosarcoma arising from the wall of the superior vena cava.

Key Words: Leiomyosarcoma, Superior vena cava syndrome