A Case of Lymphangioleiomyomatosis with Pregnancy.

Kim, Seong Ook; Kim, Min Gu; Won, Yong Hwan; Kim, Ho Cheol; Hwang, Young Sil; Kim, Jong Hwa

doi:1995.42.3.375

Tuberc Respir Dis > Volume 42(3); 1995 > Article

Case Report

Tuberculosis and Respiratory Diseases 1995;42(3):375-380.
DOI: https://doi.org/10.4046/trd.1995.42.3.375 Published online June 1, 1995.

A Case of Lymphangioleiomyomatosis with Pregnancy.

Seong Ook Kim, Min Gu Kim, Yong Hwan Won, Ho Cheol Kim, Young Sil Hwang, Jong Hwa Kim

¹Department of Internal Medicine, College of Medicine, Gyeongsang National University, Chinju, Korea.
²Department of Obstetrics & Gynecology, College of Medicine, Gyeongsang National University, Chinju, Korea.

Abstract

The lymphangioleiomyomatosis(LAM) is a rare disorder, which afflicts mainly young woman of childbearing age, characterized by proliferation of immature smooth muscle cell in the lymphatics. We experienced a case of LAM in 26-years-old pregnant woman, confirmed pathologically by inguinal lymph node biopsy. She has suffered from exertonal dyspnea and dry coughing. The symptoms and chest X-ray were aggravated with pregnancy, but improved after delivery with two times of pregnancy. The chest X-ray showed diffuse reticulonodular infiltration and chest HRCT showed diffuse scattered tiny thin-walled cyst of lung parenchyma. We noted chylous ascites of which triglyceride level is 396 mg/dl. After delivery, the symptoms were getting better. We treated with medroxyprogesterone and planned close observation and follow-up.

Key Words: Lymphangioleiomyomatosis, Pregnancy, Chylous ascites