A case report of unilateral absence of left pulmonary artery.

Lee, Jae Ung; Park, Ik Soo; Shin, Dong Ho; Park, Sung Soo; Lee, Jung Hee; Jeon, Seok Chol; Seo, Heung Suk

doi:1992.39.6.548

Tuberc Respir Dis > Volume 39(6); 1992 > Article

Case Report

Tuberculosis and Respiratory Diseases 1992;39(6):548-553.
DOI: https://doi.org/10.4046/trd.1992.39.6.548 Published online December 1, 1992.

A case report of unilateral absence of left pulmonary artery.

Jae Ung Lee¹, Ik Soo Park¹, Dong Ho Shin¹, Sung Soo Park¹, Jung Hee Lee¹, Seok Chol Jeon², Heung Suk Seo²

¹Department of lnternal Medicine, College of Medicine, Hanyang University, Seoul, Korea
²Department of Radiology, College of Medicine, Hanyang University, Seoul, Korea

Abstract

The Unilateral absence of a pulmonary artery (UAPA) is an uncommon congenital anomaly Approximately 160 cases have been reported in the literature since Frantzel’s first report in 1968. Most of the patients with UAPA are asymptomatic but some patients may suffer from recurrent respiratory infections, hemoptysis, or pulmonary hypertension. The diagnosis could be suspected from the chest roentgenogram and lung scan, and definitely confirmed by pulmonary angiography. We experienced a case of UAPA in a 39-year-old male with the recurrent hemoptysis. Chest X.ray revealed that the left lung volume was moderately decreased and the heart and mediastinum were displaced to the left side. Lung perfusion scan showed that the left lung was not perfused. Pulmonary angiography revealed the absence of the left main pulmonary artery. Aortic arch and descending aorta on aortogram were right sided. Blood supply to the left lung was originated from numerous systemic collaterals from intercostal and brachiocephalic origin. No other intrinsic or internal abnormalities of the cardiac chambers were noted.

Key Words: Unilateral absence of pulmonary artery (UAPA)