A case of pulmonary lympgangioleiomyomatosis. |
Sung Yi Kang1, Ki Heon Yoon1, Jee Hong Yoo1, Hong Mo Kang1, Moon Ho Yang2 |
1Department of Internal Medicine, College of Medicine, Kyung Hee University, Seoul, Korea 2Department of Pathology, College of Medicine, Kyung Hee University, Seoul, Korea |
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Abstract |
Pulmonary lymphangioleiomyomatosis is a rare disease, prevalent in women of reproductive age, and characterized by proliferation of atypical smooth muscle in the lung. A 44-year-old woman with pulmonary lymphangioleiomyomatosis was presented. Chest radiographs showed diffuse increased reticulonodular infiltrations on the almost entire lung and high resolution CT illustrated multiple. well defined cystic lesions which were distributed diffusely through the lung. Histologic confirmation of lymphangioleiomyomatosis was made upon open lung biopsy. Treatment with methylprogesterone was initiated. |
Key Words:
Lymphangioleiomyomatosis, Lung, Open lung biopsy |
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