| Pulmonary Features of Hyperimmunoglobulin E (Job's)syndrome. |
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Byoung Ju Min, Jea Seung Shin, In Sung Lee, Young Kyoo Shin |
1Department of Thoracic and Cardiovascular Surgery, Korea University College of Medicine, Seoul, Korea.
2Department of Pediatrics, Korea University College of Medicine, Seoul, Korea. |
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| Abstract |
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Hyperimmunoglobulin E syndrome, otherwise known as Job's syndrome, is an immune disorder characterized by an abnormal elevation of the circulating immunoglobulin E level, and recurrent infections of the skin and sinopulmo nar tract. The syndrome has various ppulmonary featurea, e.g., pneumonia, pneumatocele, pneumothorax, lung abscesses and empyema. We report a case of hyperimmunoglobulin E syndrome, with various respiratory clinical manifestation. Medical therapy, including prophylactic antibiotics, has been the cornerstone for the treatment of hyperimmunoglobulin E syndrome. Even if surgical intervention is required, minimal pulmonary parenchymal resection is recommended. |
| Key Words:
Immunologic diseases, Immunologic deficiency syndromes, Phagocyte bactericidal dysfunction, Hyperimmunoglobulin E-recurrent infection syndrome, Job's syndrome |
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